To examine: Whether the statement “Individuals born with PKU who adhere to an adequate, low-phenylalanine diet during childhood and later in life tend to develop normally or at levels that are somewhat below normal” is true or false Introduction: Phenylketonuria (PKU) is an inherited disorder of amino acid metabolism that results in decreased metabolism of the amino acid phenylalanine due to the deficiency of enzyme, phenylalanine hydroxylase. High level of phenylalanine impairs nerve functions and also interferes with amino acid transport. It can cause intellectual disability, behavioral problem, mental disorders, and seizures in an individual if untreated.

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Chapter 3, Problem 22RQ

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To examine: Whether the statement “Individuals born with PKU who adhere to an adequate, low-phenylalanine diet during childhood and later in life tend to develop normally or at levels that are somewhat below normal” is true or false

Introduction: Phenylketonuria (PKU) is an inherited disorder of amino acid metabolism that results in decreased metabolism of the amino acid phenylalanine due to the deficiency of enzyme, phenylalanine hydroxylase. High level of phenylalanine impairs nerve functions and also interferes with amino acid transport. It can cause intellectual disability, behavioral problem, mental disorders, and seizures in an individual if untreated.

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