Following is the structural formula of ganglioside GM, a macromolecular gly- colipid (meaning that it contains lipid and monosaccharide units joined by glycosidic bonds). (b) Но CH,OH (d) HO CH,OH (f) NH CH,OH OH (a) C=0- OCH,CHCHCH=CH(CH,)12CH3 OH ОН Но. ČH3 (c) NHC(CH,) 16CH3 (e) НО ОН OH НООС NH HO C=O CH3 Ganglioside GM or Tay-Sachs ganglioside In normal cells, this and other gangliosides are synthesized continuously and degraded by lysosomes, which are cell organelles containing digestive enzymes. If pathways for the degradation of gangliosides are inhibited, the gangliosides accumulate in the cen- tral nervous system, causing all sorts of life-threatening consequences. In inherited diseases of ganglioside metabolism, death usually occurs at an early age. Diseases of ganglioside metabolism include Gaucher's disease, Niemann-Pick disease, and Tay- Sachs disease. Tay-Sachs disease is a hereditary defect that is transmitted as an au- tosomal recessive gene. The concentration of ganglioside GM, is abnormally high in this disease because the enzyme responsible for catalyzing the hydrolysis of glycosidic bond (b) is absent.

Q: How many diastereomers of this monosaccharide are there? Assume that the monosaccharide is of…

A: The type of isomerism where isomers have same molecular formula but different orientation in…

Q: The monosaccharide shown below polymerizes to form a polysaccharide where each sugar residue is…

A: Cellulose is the most important structural component of the cell wall of plants. It is a linear…

Q: Draw the Haworth structure of the tetrasaccharide:

A:

Q: Glucose and fructose are reducing sugars. Sucrose, or table sugar, is a disaccharide consisting of…

A: Carbohydrates are the energy-producing biomolecules commonly known as sugars that are can be…

Q: The galactose residue is linked to glucose via a/an [alpha linkage, beta linkage]  and the glucose…

A: Trisaccharide refers to a molecule that contains three monosaccharide units. A monosaccharide unit…

Q: gar is pois

A: Sugar is a form of soluble carbohydrate that is sweet and is used in food items. Variety of sugar…

Q: Draw the open form of the monosaccharides of digitoxin/digoxin?

A: Digitoxin is a cardiac glycoside, a type of chemical molecule generated from the leaves of Digitalis…

Q: Write two examples of Glycosaminoglycan.

A: Glycosaminoglycan is tandem repeats of Amino sugar and uronic acids.

Q: Assume you could make a trisaccharide by covalently joining xylose (C5H10O5) , xylose (C5H10O5) and…

A: Dehydration: Loss of water(H2O) molecule Asked : Trisaccharide chemical formula

Q: what is the name of the monosaccharide A?

A: The name of the Monosaccharide A is GALACTOSE.  The structure differs from glucose at the fourth…

Q: Ribose is know as this type of sugar because of the number of Carbon atoms it possesses.

A: Question - Ribose is know as this type of sugar because of the number of Carbon atoms it possesses.

Q: finish the systematic name of the disaccharide lactose

A: Disaccharides are one of the types of carbohydrate molecules containing two units of…

Q: Discuss the ease of hydrolysis (break down) for each of the 4 polysaccharides (glycogen, amylose,…

A: Food is an important energy source to carry on the normal physiological functions of the body.…

Q: How would a monosaccharide with 7 C atoms & a ketone group be classified? Choose your answer from…

A: Carbohydrates are the hydrates of carbon. Carbohydrates are the primary energy source for most…

Q: From these sentences answer YES or NO,  1. Are ALL ketoses are optically active?

A: Carbohydrates or carbs are maconutrient consisting of Carbon, hydrogen and oxygen atoms. In nature…

Q: Draw the Gentiobiose: 2 Glucose, beta-(1,6)

A: Gentiobiose is a disaccharide composed of two subints of D-glucose via β(1-6) linkage. It is soluble…

Q: Write definition of α- and β-anomers of monosaccharides.

A: Monosaccharides are monomers that form the polymer polysaccharides (carbohydrates). A monosaccharide…

Q: Glycosaminoglycans have the following characteristics except—     Each disaccharide unit contains a…

A: Glycosaminoglycans: These are simply called as GAGs which are found in mammalian tissues. They are…

Q: How many carbon atoms are there in fructose? In sucrose?

A: Sugars are sweet-tasting carbohydrates that are the primary source of energy in food. They can be…

Q: Match the concepts to their corresponding definitions or examples. Match each item to a choice:…

A:

Q: Why is it impossible for humans to digest food thatcontains cellulose?

A: Cellulose can be defined as the molecule which consist of hundreds  and  thousands  elements known…

Q: CH,OH CH,OH OH OH ÓH ÓH ÓH

A: Polysaccharides are composed of monosaccharides that re connected by glycosidic linkages.

Q: Consider the following statements: (1) Complete hydrolysis of a disaccharide produces only…

A: Monosacharides are the simple sugars which are named on the basis of number of carbon atoms in the…

Q: What is the structural difference between the monosaccharides glucose and galactose?

A: Monosaccharides are the simple sugar, that can not be hydrolyzed. Monosaccharides have the general…

Q: Which of the following disaccharides produces two different monosaccharides upon hydrolysis?…

A: Disaccharides are the Carbohydrate molecules made up of two monosacharide units. The monosacharides…

Q: Name the three different polysaccharides. explain their structure (and their differences) and where…

A: Polysaccharides are ubiquitous in nature. Polysaccharides are polymers with hundreds or thousands…

Q: There are several sugars along with fructose and glucose that are isomeric, name them

A: The question asked for a list of sugars that are isomeric to fructose and glucose. Isomers are…

Q: OH H. OH ОН OH O A -O- H. H. OH Но O. HI

A: Trisaccharide is made up of three monosaccharide units, it is a type of oligosaccharide. In…

Q: hain elongation of monosaccharides can be done in the laboratory thru Ruff reaction.  True  False

A: The Ruff degradation is the process of converting an aldose to its analogue with one less carbon…

Q: How many chiral carbon atoms are in glucose in the cyclic form?

A: The chiral carbon is defined as carbon atom attached with four different types or group of atoms.

Q: What is the relationship between the following monosaccharides (enantiomers, diastereomers, or…

A: Enantiomers are stereoisomers that are mirror images of each other. The D and L forms of a sugar are…

Q: Lactose is the sugar component of milk, which is why it is referred to as "milk sugar." It is…

A: Carbohydrates are the most essential biomolecule and the primary source of energy in many organisms.…

Q: Identify the products of the digestion/hydrolysis reactions involving the following polymers (hint:…

A: The fundamental components that make up polymers, known as monomers, are tiny, repeating units that…

Q: We are consuming a lot of polymers in our foods and only some monomers. The polymers we ingest must…

A: Introduction: The mechanism by which the ingested complex food substances are broken down by…

Q: Classify each monosaccharide by using the type of carbonyl group and the number of carbons in the…

A: Detailed explanation: Part 1 of 3: Classify galactose Galactose has the chemical formula C6H12O6,…

Metabolic pathways

Metabolism is defined as the group of life-supporting, enzyme-mediated chemical reactions in organisms. A metabolic pathway is a set of these chemical reactions that involve anabolism (synthesis of complex biomolecules) and catabolism (breakdown of biomolecules into small molecules) that occur inside a cell. Metabolites are the reacting substances, products, and intermediate substances of an enzymatic process that are altered by a series of chemical events catalyzed by enzymes.