Following is the structural formula of ganglioside GM, a macromolecular gly- colipid (meaning that it contains lipid and monosaccharide units joined by glycosidic bonds). (b) Но CH,OH (d) HO CH,OH (f) NH CH,OH OH (a) C=0- OCH,CHCHCH=CH(CH,)12CH3 OH ОН Но. ČH3 (c) NHC(CH,) 16CH3 (e) НО ОН OH НООС NH HO C=O CH3 Ganglioside GM or Tay-Sachs ganglioside In normal cells, this and other gangliosides are synthesized continuously and degraded by lysosomes, which are cell organelles containing digestive enzymes. If pathways for the degradation of gangliosides are inhibited, the gangliosides accumulate in the cen- tral nervous system, causing all sorts of life-threatening consequences. In inherited diseases of ganglioside metabolism, death usually occurs at an early age. Diseases of ganglioside metabolism include Gaucher's disease, Niemann-Pick disease, and Tay- Sachs disease. Tay-Sachs disease is a hereditary defect that is transmitted as an au- tosomal recessive gene. The concentration of ganglioside GM, is abnormally high in this disease because the enzyme responsible for catalyzing the hydrolysis of glycosidic bond (b) is absent.

Q: How many diastereomers of this monosaccharide are there? Assume that the monosaccharide is of…

A: The type of isomerism where isomers have same molecular formula but different orientation in…

Q: Name two simple carbohydrates, two storage carbohydrates, and a structural carbohydrate.

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Q: Glucose and fructose are reducing sugars. Sucrose, or table sugar, is a disaccharide consisting of…

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Q: The galactose residue is linked to glucose via a/an [alpha linkage, beta linkage]  and the glucose…

A: Trisaccharide refers to a molecule that contains three monosaccharide units. A monosaccharide unit…

Q: Define oligosaccharides.

A: Oligosaccharides are any carbohydrate of from 3 to 6 units of simple sugars (monosaccharides) . A…

Q: Draw and name the commonmonosaccharides using structuralformulas.

A: Monosaccharides, also known as simple sugars, are the most common units of carbohydrates and the…

Q: gar is pois

A: Sugar is a form of soluble carbohydrate that is sweet and is used in food items. Variety of sugar…

Q: Write two examples of Glycosaminoglycan.

A: Glycosaminoglycan is tandem repeats of Amino sugar and uronic acids.

Q: List four monosaccharides? Where are they located?

A: A monosaccharide is that the most elementary kind of carbohydrates. Monosaccharides will be combined…

Q: Recognize the modified monosaccharides present in naturally occurring polysaccharides and their…

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Q: Ribose is know as this type of sugar because of the number of Carbon atoms it possesses.

A: Question - Ribose is know as this type of sugar because of the number of Carbon atoms it possesses.

Q: finish the systematic name of the disaccharide lactose

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Q: What are polysaccharides? Classify. Give examples.

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Q: List several examples of important monosaccharides andpolysaccharides.

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Q: Identify the modified monosaccharides found in naturally occurring polysaccharides and identify the…

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Q: Glycosaminoglycans have the following characteristics except—     Each disaccharide unit contains a…

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Q: Why are polysaccharides (e.g. starch) not soluble in cold water but are soluble in warm water?

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Q: Briefly describe the structural differences for each pair listed: A) Glycogen and Cellulose   B)…

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Q: How many carbon atoms are there in fructose? In sucrose?

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Q: Why is it impossible for humans to digest food thatcontains cellulose?

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Q: CH,OH CH,OH OH OH ÓH ÓH ÓH

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Q: Which of the following disaccharides produces two different monosaccharides upon hydrolysis?…

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Q: Do structural polysaccharides typically have extensive hydrogen bonding?

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Q: There are several sugars along with fructose and glucose that are isomeric, name them

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Q: What disaccharide does enzyme lactase digest? What two products (monosaccharides) is this…

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Q: Name four important monosaccharides and tell where each occurs in nature.

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Q: there a relationship between the structure and function of the di-, oligo-, and polysaccharides

A: Asked : If there is relationship between structure and function of given carbohydrates

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Q: Define monosaccharide

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Q: Define polysaccharide

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Q: Which of the two polysaccharides contains branched chains of the monosaccharides?

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Q: Write the name of different types of homopolysachharide.

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Metabolic pathways

Metabolism is defined as the group of life-supporting, enzyme-mediated chemical reactions in organisms. A metabolic pathway is a set of these chemical reactions that involve anabolism (synthesis of complex biomolecules) and catabolism (breakdown of biomolecules into small molecules) that occur inside a cell. Metabolites are the reacting substances, products, and intermediate substances of an enzymatic process that are altered by a series of chemical events catalyzed by enzymes.