Reaction between glycine and isovaleric acid. Concept introduction: Isovaleric acidemia is an autosomal recessive disorder which results in the abnormal metabolism of the leucine amino acid. It causes the accumulation of organic acid, which leads to acidemia. During this disorder, tissues are harmed, and sometimes it may also lead to the death of the person.

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Chapter 24, Problem 19P

Interpretation Introduction

Interpretation:

Reaction between glycine and isovaleric acid.

Concept introduction:

Isovaleric acidemia is an autosomal recessive disorder which results in the abnormal metabolism of the leucine amino acid. It causes the accumulation of organic acid, which leads to acidemia. During this disorder, tissues are harmed, and sometimes it may also lead to the death of the person.

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