A baby boy was seen at the hospital because his urine had of a musty odour. Large amounts of an amino acid were present in his urine. In addition, a compound (comnpound I) was isolated from the urine in substantial amounts which, when incubated with NADH and lactate dehydrogenase, gave rise to compound II (shown below). Compound II: ОН OH a. Name and draw the structure of compound I? b. Which class of reaction is involved in the formation of compound I from the amino acid that is present in the urine? c. What is the likely metabolic block in the child?

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Metabolic pathways

Metabolism is defined as the group of life-supporting, enzyme-mediated chemical reactions in organisms. A metabolic pathway is a set of these chemical reactions that involve anabolism (synthesis of complex biomolecules) and catabolism (breakdown of biomolecules into small molecules) that occur inside a cell. Metabolites are the reacting substances, products, and intermediate substances of an enzymatic process that are altered by a series of chemical events catalyzed by enzymes.