In patient with Maple Syrup Urine Disease, what specific amino acids should be not used in order to ameliorate the existing diseases condition? Why have you selected these amino acids?

Biochemistry
9th Edition
ISBN:9781319114671
Author:Lubert Stryer, Jeremy M. Berg, John L. Tymoczko, Gregory J. Gatto Jr.
Publisher:Lubert Stryer, Jeremy M. Berg, John L. Tymoczko, Gregory J. Gatto Jr.
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In patient with Maple Syrup Urine Disease, what specific amino acids should be not used in order to ameliorate the existing diseases condition? Why have you selected these amino acids?

 

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Maple syrup urine disease is an autosomal recessive metabolic disorder affecting branched-chain amino acids. The condition get its name from the distinctive sweet odor of affected infant's urine, particularly prior to diagnosis and during times of acute illness.

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